J Cerebrovasc Endovasc Neurosurg.  2021 Jun;23(2):85-98. 10.7461/jcen.2021.E2020.09.004.

The Top-100 most cited articles on Moyamoya disease: A bibliometric analysis

• Alkhaibary A
• Almutairi OT
• Elarjani T
• Alnefaie N
• Alhussinan MA
• Bafaquh M
• Alturki AY

• KMID: 2517021
• DOI: http://doi.org/10.7461/jcen.2021.E2020.09.004

Abstract

Objective
Moyamoya disease (MMD) is a progressive steno-occlusive cerebrovascular phenomenon with unknown pathogenesis. Considering the abundance of articles addressing Moyamoya disease, a detailed analysis concerning the publication trends is of paramount importance. The aim of the study is to report the current knowledge of the top-100 most cited articles on Moyamoya disease in the literature.
Methods
A non-time restricted keyword-based search was performed in June 2020 using the Scopus database. The search keywords included the following: “Moyamoya”, “Moyamoya disease”, and “Moyamoya syndrome”. The search result was used to rank the articles based on their citation count. The top-100 most-cited articles were obtained and classified into seven categories.
Results
A total of 3,543 articles on Moyamoya disease were published between 1955 and 2020. The Top-100 articles were published between 1977 and 2016 with a total of 16,119 citations, per year, and 7.23% rate of self-citation. The 1990s was the most productive decade (N=42). The most contributing country to the list was Japan (N=60). Stroke was the most active journal (N=23). Houkin, K., a Japanese neurosurgeon, was the most prolific author (N=15).
Conclusions
Moyamoya disease has been extensively investigated in the literature throughout the years. The majority of articles published in the literature were addressing the surgical management and clinical outcome. Authors from neurosurgical backgrounds were the most active contributors to the field of Moyamoya disease.

Keyword

Moyamoya disease; Moyamoya syndrome; Stroke

Figure

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  Fig. 1. Publication trends of the top-100 most cited articles on Moyamoya disease between 1977-2016.

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  Fig. 2. Categorical distribution of Moyamoya disease in the top-100 cited articles.

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  Fig. 3. The country of origin of the articles on Moyamoya disease in the top-100 cited articles.

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  Fig. 4. Affiliated institutes contributing to the highest cited articles on Moyamoya disease.

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  Fig. 5. The top journals publishing articles on Moyamoya disease and their corresponding impact factor, Journal’s SNIP, Journal’s SJR. SNIP, Source Normalized Impact Per Paper; SJR, Journal’s SCImago Journal Rank.

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  Fig. 6. Affiliated institutes contributing to the highest cited articles on Moyamoya disease.

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