Neonatal Med.  2021 May;28(2):72-76. 10.5385/nm.2021.28.2.72.

Intussusception and Jejunal Atresia Caused by an Ectopic Pancreas in a Newborn

• Kim HS
• Lee SY
• Han SH
• Nam SH
• Jo CK
• Kim MJ

• KMID: 2516488
• DOI: http://doi.org/10.5385/nm.2021.28.2.72

Abstract

Ectopic pancreas is defined as an abnormally located pancreatic tissue not sufficiently connected with the normal pancreas, which rarely occurs in neonates. To our knowledge, only a few cases of ectopic pancreas have been reported in newborns in South Korea. We report a case of ectopic pancreas as the cause of intussusception and jejunal atresia in a newborn. This clinical association is extremely rare, and this is the first report in South Korea.

Keyword

Ectopic pancreas; Intussusception; Intestinal atresia; Newborn

Figure

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  Figure 1. Abdominal radiograph shows multiple small bowel dilatation and a gasless rectum.

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  Figure 2. A small bowel intussusception is detected in the abdominal ultrasound.

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  Figure 3. (A) Exploratory laparotomy reveals the presence of jejunojejunal intussusception (arrow). (B) A hemorrhagic mass and jejunal atresia are found in the distal jejunum (arrow).

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  Figure 4. (A) A hemorrhagic mass-like lesion is detected on the jejunal wall (black arrow). Squamous metaplasia is also observed (H&E stain, ×0.5). (B) Histological examination of the jejunal mass demonstrates the presence of pancreatic ducts (yellow arrows) (H&E stain, ×5.0). (C) The tissue section reveals a pancreatic acinus with a heterotopic pancreas (yellow arrows) (H&E stain, ×5.0).

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