J Korean Assoc Oral Maxillofac Surg.  2021 Apr;47(2):141-144. 10.5125/jkaoms.2021.47.2.141.

Osteopathia striata in the mandible with cranial sclerosis: a case report and review of the literature

• Jagtap R
• Garrido MB
• Hansen M

• KMID: 2515313
• DOI: http://doi.org/10.5125/jkaoms.2021.47.2.141

Abstract

Osteopathia striata with cranial sclerosis (OS-CS) is a bone dysplasia characterized by a linear striated pattern of sclerosis, especially in the long bones, and cranial sclerosis. It has variable clinical findings but distinctive radiological findings. Multiple oral and dental findings have been associated with this disease and can be seen during dental and/or medical imaging of the head and neck. Dentists and clinicians must be familiar with these signs to differentiate them from pathosis or erroneous radiographs. In the following case, we present a patient with OS-CS that presented at The University of Florida College of Dentistry with multiple craniofacial manifestations of this syndrome that were seen on a panoramic radiograph, which is one of the most commonly requested radiographs by dentists.

Keyword

Osteopathia striata with cranial sclerosis; Oral manifestation; Oral and maxillofacial radiology; Oral surgery

Figure

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  Fig. 1 A. In 2016, there is an increased bone mass of the cranium displayed as multiple lobulated, homogeneous radiopaque entities superimposing the maxilla, temporomandibular joints, sphenoid, and temporal bones. B. In 2017, the visualized cortical outline of the maxilla and mandible appeared dense, thickened and sclerotic.

Reference

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