J Korean Orthop Assoc.  1975 Sep;10(3):314-319. 10.4055/jkoa.1975.10.3.314.

Congenital Indifference to Pain: Report of a Case

• Lee SH
• Yang YS
• Lee DY

• KMID: 2471434
• DOI: http://doi.org/10.4055/jkoa.1975.10.3.314

Abstract

The syndrome of congenital indifference to pain is attributed to an abnormal affective response rather than to defective perception. It consists of failure to react normally to noxious stimuli and usually occurs a isolated sensory abnormality. Sensory apparatus of the patient is intact as far as can be determined. We experienced a rare case of congenital indifference to pain with decreased sweating and positive family history.

MeSH Terms

Humans
Pain Insensitivity, Congenital*
Sweat
Sweating

Figure

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  寫眞 1. 右側 繣厕節㢨 㴔⪤ 㝻㏃, 㦈䍸䍀⧫匄 兩側 獟樤節㢨 佌䍸䍀⧫㢌 䌌㢈䴜.

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  寫眞 2. ⨀侣匄 frenulum 㢨 傷痕{生 瑶化

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  寫眞 3. 妹㢨 㹰, 左側姆指㢨 瑶形㢌 ䷸㨰 䖌䴜.

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  寫眞 4. Iodine-strach 發汗檢查. 厌叫㢈(左)㣀 瑶綎㢌 匀㏐䯤 反梞 ⦨㡰(右)䵬 㟼⨀䍀⦬吀 㨺䴜.

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  寫眞 5. Histamin axon reflex test. 右側前炷漘 (⦬㽌 JL) 㨰 wheal 匄 axon flare 吀 佨⽀佔䴜.

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  寫眞 6. 兩側繣樤節㢨 單純 X線⦤㧿㹴協

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  寫眞 7. 右側繣樤節 手瞭所癵. ᄎ纁敘 㢨㇟匄㢨 不全癒 合䯤 敘折㢼 䌄㷨 㡸䴜.

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  寫眞 8. 左側时樤節 劰㟫㷨㷠勯千. 慅湷䚄 施瞴⪨㙀 㪶 匠 手瞭中㢌䴜. 息翻䵬 不安⪤ 瞘情㢄䀰 級瘤 㵜䠔㤴 䌌㢌㙀䵬 㪶䵬䴜.

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  寫眞 9. 瀃疚中 發癵䯤 右側纬敘 䏱 徘敘㢨 敘折

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  寫眞 10. 瀃疚中 發生⪤ 左側 汪敘㢨 敘楘炎. 患漘吀 䊀㩌 㧔䢄㡸䴜.

Reference

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