J Cardiovasc Imaging.  2019 Oct;27(4):286-287. 10.4250/jcvi.2019.27.e37.

A Rare Case of Cardiac Involvement in Rosai-Dorfman Disease

• Tsigaridas N
• Mantzoukis S
• Mpakas K
• Troganis E
• Patsouras

• KMID: 2468357
• DOI: http://doi.org/10.4250/jcvi.2019.27.e37

Abstract

No abstract available.

MeSH Terms

Histiocytosis, Sinus*

Figure

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  Figure 1 Transthoracic echocardiogram: four chamber view showing a mass in the right atrium and the interatrial septum before (A) and after contrast (B) injection. (C) A subcostal view showing contrast enhancement of the mass.

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  Figure 2 (A) Transesophageal echocardiographic 2D bicaval view showing the relation of the mass to the interatrial septum and the orifices of the superior and the inferior vena cava and (B) 3D view of the right atrium showing the relation of the mass to the interatrial septum and the orifices of IVC and CS. (C) Chest CT with contrast administration performed 6 months before presentation showing the mass virtually encircling the right atrial cavity. CS: coronary sinus, IAS: interatrial septum, IVC: inferior vena cava.

Reference

1. Rosai J, Dorfman RF. Sinus histiocytosis with massive lymphadenopathy. A newly recognized benign clinicopathological entity. Arch Pathol. 1969; 87:63–70.

2. Dalia S, Sagatys E, Sokol L, Kubal T. Rosai-Dorfman disease: tumor biology, clinical features, pathology, and treatment. Cancer Control. 2014; 21:322–327.

3. Heidarian A, Anwar A, Haseeb MA, Gupta R. Extranodal Rosai-Dorfman disease arising in the heart: clinical course and review of literature. Cardiovasc Pathol. 2017; 31:1–4.