J Korean Soc Radiol.  2019 Jul;80(4):783-787. 10.3348/jksr.2019.80.4.783.

Congenital Embryonal Rhabdomyosarcoma of the Extraperitoneal Pelvic Space with a Prenatal Onset: A Case Report

• Yoo SJ
• Kang BK
• Kim M
• Song SY
• Koh BH

• KMID: 2457458
• DOI: http://doi.org/10.3348/jksr.2019.80.4.783

Abstract

Rhabdomyosarcoma is the most common pediatric soft tissue malignancy, however, extraperitoneal origin of the tumor is rare and prenatal onset of the tumor is even more rare. In this article, we report a radiologic finding of a case of embryonal rhabdomyosarcoma at the extraperitoneal pelvic space in a newborn.

MeSH Terms

Humans
Infant, Newborn
Pelvic Neoplasms
Rhabdomyosarcoma
Rhabdomyosarcoma, Embryonal*

Figure

• 

  Fig. 1 Embryonal rhabdomyosarcoma of the extraperitoneal pelvic space in a newborn infant. A. Initial abdomen ultrasonography at the level of the lower abdomen in the supine position shows a large heterogeneously hyperechoic mass (arrow) located posterior to the urinary bladder (arrowhead). B. The sagittal T2-weighted image shows a 7-cm heterogeneously hyperintense soft tissue mass in the extraperitoneal pelvic space. The urinary bladder (arrow) and the uterus (arrowhead) are displaced superiorly, and the vagina (empty arrow) is displaced posteriorly. C. The axial T2-weighted image shows the mass directly invading the posterior wall of the urinary bladder (arrowhead). D, E. The mass in the extraperitoneal pelvic space shows low signal intensity on the axial T1-weighted image (D) and heterogeneous enhancement with internal necrosis on the axial contrast-enhanced fat-saturated T1-weighted image (E).

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