J Cardiovasc Imaging.  2019 Jul;27(3):230-233. 10.4250/jcvi.2019.27.e34.

Sigmoid Septum and Aberrant Calcified Papillary Muscle in the Setting of Advanced Hypertrophic Cardiomyopathy: An Unusual Life-threatening Coalescence

• Hallo C
• Kottiech S
• Castillo J

• KMID: 2456860
• DOI: http://doi.org/10.4250/jcvi.2019.27.e34

Abstract

No abstract available.

Keyword

Papillary muscles; Hypertrophic cardiomyopathy; Heart septum; Echocardiography

MeSH Terms

Cardiomyopathy, Hypertrophic*
Colon, Sigmoid*
Echocardiography
Heart Septum
Papillary Muscles*

Figure

• 

  Figure 1 Mid-esophageal long axis view shows severe focal hypertrophy of the ventricular septum (arrow head) with an 82° angulation between the basal portion of the ventricular septum and the ascending aorta (line), as well as an accessory calcified papillary muscle.

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  Figure 2 Transgastric long axis view shows an aberrant accessory papillary muscle (arrow head).

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  Figure 3 Three-dimensional transesophageal echocardiography demonstrates an abnormal attachment of an aberrant papillary muscle (arrow head). AL: anterior leaflet of mitral valve, APM: aberrant papillary muscle, LVOT: left ventricular outflow tract, PL: posterior leaflet of mitral valve.

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  Figure 4 Mid-esophageal long axis view reveals severe systolic anterior motion of the mitral valve and obstruction of the left ventricular outflow tract.

Reference

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