Obstet Gynecol Sci.
2019 Sep;62(5):367-370. 10.5468/ogs.2019.62.5.367.
Currarino syndrome in an adult woman
- Affiliations
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- 1Department of Obstetrics and Gynecology, Cheil General Hospital and Women's Healthcare Center, College of Medicine, Dankook University, Seoul, Korea.
- 2Department of Obstetrics and Gynecology, Yonsei University College of Medicine, Seoul, Korea.
- 3Department of Obstetrics and Gynecology, CHA Gangnam Medical Center, CHA University, Seoul, Korea.
- 4Department of Radiology, Cheil General Hospital and Women's Healthcare Center, College of Medicine, Dankook University, Seoul, Korea.
- 5Department of Obstetrics and Gynecology, Hallym University Kangdong Sacred Heart Hospital, Seoul, Korea.
- 6Department of Obstetrics and Gynecology, Konkuk University School of Medicine, Seoul, Korea. joyfulplace@hanmail.net
- KMID: 2456834
- DOI: http://doi.org/10.5468/ogs.2019.62.5.367
Abstract
- Currarino syndrome is a hereditary disease characterized by the triad of sacral agenesis, anorectal malformation, and presacral mass. Most patients are diagnosed in childhood, and this condition rarely manifests in adulthood. In women, gynecological malformations associated with Currarino syndrome have been reported, such as bicornuate uterus, rectovaginal fistula, and septate uterus. We present a rare case of a 29-year-old woman with a suspected pelvic mass who was diagnosed with Currarino syndrome.
Figure
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Fig. 1 Pelvic magnetic resonance image shows (A) a partial septate uterus (1.7 cm of the muscular septum) with right anterior displacement secondary to a massively distended rectum. (B) Right-sided anterior sacral meningocele (arrow) is observed.
Fig. 2 Abdominal radiograph shows sacral hypogenesis (scimitar sacrum) and a massively distended sigmoid colon filled with feces.
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