Investig Magn Reson Imaging.  2019 Jun;23(2):172-174. 10.13104/imri.2019.23.2.172.

Recurrent Painful Ophthalmoplegic Neuropathy: a Case Report

• Park JH
• Lee HK
• Koh MJ
• Oh JH
• Park SJ

• KMID: 2452533
• DOI: http://doi.org/10.13104/imri.2019.23.2.172

Abstract

Upon review, it is noted that recurrent painful ophthalmoplegic neuropathy (RPON) is a rare neurological syndrome characterized by recurrent unilateral headaches and painful ophthalmoplegia of the ipsilateral oculomotor nerve. As seen on brain MRI, thickening and enhancement of the oculomotor cranial nerve can be observed in these cases. We experienced a case of RPON in an adult patient who showed thickening and enhancement of the oculomotor nerve on gadolinium-enhanced 3D-FLAIR image. The authors report a case of RPON with a review of the literature.

Keyword

Oculomotor nerve disease; Paralysis; Headache; Magnetic resonance imaging

MeSH Terms

Adult
Brain
Cranial Nerves
Headache
Humans
Magnetic Resonance Imaging
Oculomotor Nerve
Oculomotor Nerve Diseases
Ophthalmoplegia
Paralysis

Figure

• 

  Fig. 1 Brain MRI of a 28-year-old man with recurrent headaches and right oculomotor paresis. Gadolinium-enhanced T1-weighted axial (a) and coronal (b) images show thickening and homogeneous enhancement of the right oculomotor nerve (arrows) at the cisternal segment, as noted and compared with the non-enhanced T1-weighted image (c). Gadolinium-enhanced 3D-FLAIR axial (d, e) and coronal (f) images show evident thickening and heterogeneous enhancement of the right oculomotor nerve (arrows) at the cisternal segment at the same plane.

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