Korean J Thorac Cardiovasc Surg.  2019 Apr;52(2):100-104. 10.5090/kjtcs.2019.52.2.100.

Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient

• Shih BC
• Lim JH
• Min J
• Kim ER
• Kwak JG
• Kim WH

• KMID: 2447609
• DOI: http://doi.org/10.5090/kjtcs.2019.52.2.100

Abstract

Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.

Keyword

Shone's complex; Bicuspid aortic valve; Parachute mitral valve; Extraanatomic bypass; Aortic coarctation

MeSH Terms

Adult*
Aortic Coarctation
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Constriction, Pathologic
Diagnosis
Female
Follow-Up Studies
Heart
Heart Defects, Congenital*
Humans
Mitral Valve