J Korean Orthop Assoc.  1988 Dec;23(6):1576-1580. 10.4055/jkoa.1988.23.6.1576.

Congenital Pseudarthroses of Both Bones of the Forearm Associated with Neurofibromatosis: A Case Report

• Lee SK
• Chang H
• Shin KS

• KMID: 2445200
• DOI: http://doi.org/10.4055/jkoa.1988.23.6.1576

Abstract

The occurence of pseudarthroses associated with neurofibromatosis is a well documented phenomenon, with the majority of reported cases in the tibia but quite rare in forearm,Only ten cases in the English-literature and one case in Korean-literature of this lesion revealed appearing in the bones of the forearm till now. Of these, four in solitary pseudarthroses of the ulna(4.5.15), five in a solitary lesion of the radius(7.8.10.16.17), and only two cases was on the both bones of the forearm(9.14). We are presenting the case report of a Korean adult male with the clinical stigmata and a positive familial history of neurofibrormotosis who had congenital pseudarthroses of both the radius and ulna of the right forearm. Therefore, the present case is the third to be reported. We treated him with by production of an one-bone forearm using a dual a onlay bone graft positioned in neutral of supination and pronation. A stable, functional extremity with good union of pseudarthroses were encountered.

Keyword

Congenital pseudarthroses; Forearm; Neurofibromatosis; One-bone forearm

MeSH Terms

Adult
Christianity
Extremities
Forearm*
Humans
Inlays
Male
Neurofibromatoses*
Neurofibromatosis 1
Pronation
Pseudarthrosis*
Radius
Supination
Tibia
Transplants
Ulna