A Clinical Study on Basic Information about Congenital Constriction Band Syndrome

Yoon, Kang Sup; Chung, Moon Sang

Abstract

Twenty-seven patients with congenital constriction band syndrome were treated at department of orthopedic surgery, college of medicine, Seoul National University between 1981 and 1989. In order to obtain basic and fundamental information about this syndrome, we have analyzed the clinical records of those patients who were treated at our hospital with above syndrome. Analysis was based on the age at operation, sex distribution, familial history and past-medical history, prevalent sites of constricition bands, associated anomalies and methods of surgical treatments. The results were summarized as follows: l. Average age at operation was 9.3 months and the ratio of sex was 3:2 as male predominant. 2. There was no case with familial history of this syndrome, and serious medical problems of patient's mothers during pregnancy were not experienced except 4 cases who took some medication for URI. 3. The frequency of constriction band was greater distally than proximally, and 91% of these bands were noted distal to knee and elbow joint. 4. About 85% of cases were associated with other anomalies, and among them syndactylism and acral absence were most frequent. 5. For the simple constriction ring, staged excision of the ring and z-plasty of the defects seemed to be a most agreeable recommendation. And other associated anomalies of digits could be treated with combined procedures such as seperation of digits, web construction, transposition of ray, lengthening of digit, skin graft, corrective osteotomy, etc.