Brain Tumor Res Treat.  2018 Oct;6(2):86-91. 10.14791/btrt.2018.6.e15.

Secondary Aneurysmal Bone Cyst in a Craniofacial Fibrous Dysplasia: Case Report

• Lee HS
• Koh YC
• Roh HG
• Park HK
• Kim SY

• KMID: 2423980
• DOI: http://doi.org/10.14791/btrt.2018.6.e15

Abstract

Aneurysmal bone cyst (ABC) is a rare non-neoplastic bone lesion that involves mostly the long bones and vertebrae and may occur very rarely in the craniofacial bones. ABCs may occur as secondary bony pathologies in association with various benign and malignant bone tumors and with fibrous dysplasia (FD). FD is a common non-neoplastic bony pathology mostly affecting craniofacial bones. Secondary ABC occurring in craniofacial FD is extremely rare, with only approximately 20 cases reported in the literature to date. Here, we report on a case of secondary ABC in a 25-year-old woman who has had a craniofacial deformity for over 10 years and who presented to us with a rapidly growing painful pulsatile mass in the right frontal region that began over 2 months prior to admission. On thorough examination of computed tomography and magnetic resonance imaging brain scans taken at two-month interval, an aggressive, rapidly enlarging ABC, arising from the right frontal FD, was diagnosed. The patient underwent preoperative embolization followed by gross total resection of the ABC and cranioplasty. The 6-month follow up showed no recurrence of the ABC, nor was any progression of the FD noticed.

Keyword

Aneurysmal bone cysts; Fibrous dysplasia of bone; Frontal bone; Craniotomy

MeSH Terms

Adult
Aneurysm*
Bone Cysts*
Bone Cysts, Aneurysmal
Brain
Congenital Abnormalities
Craniotomy
Female
Fibrous Dysplasia of Bone
Follow-Up Studies
Frontal Bone
Humans
Magnetic Resonance Imaging
Pathology
Recurrence
Spine

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