J Korean Orthop Assoc.  1996 Apr;31(2):352-356. 10.4055/jkoa.1996.31.2.352.

Popliteal pterygium syndrome: A Case Report

• Rhee KJ
• Lee JK
• Park CH
• Woo YG
• Lee SY

• KMID: 2423614
• DOI: http://doi.org/10.4055/jkoa.1996.31.2.352

Abstract

Popliteal pterygium syndrome is rare, with 60 cases described in the literature. The syndrome includes a popliteal web extending from the ischium to the heel and other abnormalities including toenail dysplasia, deformities of the foot and toes, and oral cavity abnormalities. The main orthopedic problem is a flextion contracture of the knee and an equinus foot. We experienced a six-month-old girl with popliteal pterygium, in whom resection of abnormal fibrotic muscle belly, Achilles tendon legnthening, and Z-plastic lengthening of the skin resulted in partial correction of flexion deformity of the knee and equines contracture of the foot at one year follow-up.

Keyword

Popliteal pterygium syndrome

MeSH Terms

Achilles Tendon
Congenital Abnormalities
Contracture
Female
Follow-Up Studies
Foot
Heel
Humans
Ischium
Knee
Mouth
Nails
Orthopedics
Pterygium*
Skin
Toes