Korean J Ophthalmol.  2018 Oct;32(5):424-425. 10.3341/kjo.2017.0145.

Adult onset xanthogranuloma associated with IgG4-related disease

• Leung KC
• Ko P
• Ho CH
• Ko TC

• KMID: 2422073
• DOI: http://doi.org/10.3341/kjo.2017.0145

Abstract

No abstract available.

MeSH Terms

Adult*
Humans

Figure

• 

  Fig. 1 (A) Xanthelesmatous lesions and swelling involving bilateral eye lids. (B) Magnetic resonance imaging showed enhancement of soft tissue density in superior and lateral aspects of the left globe in the preseptal region (red arrow). (C) Histology showing diffuse infiltrate and nodular aggregates of foamy histiocytes in biopsy (×400). (D) Histology showing Touton type giant cells with histiocytic infiltration consistent with diagnosis of xanthogranulomatous disease (×400). (E) Resolution of xanthelesmatous lesions and reduced swelling after treatment with rituximab. Informed consent has been obtained from patient for treatment and publication.

Reference

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