Arch Craniofac Surg.  2018 Jun;19(2):135-138. 10.7181/acfs.2018.01704.

Forehead reconstruction with a custom-made three-dimensional titanium implant in a Parry-Romberg syndrome patient

• Kim JY
• Jung BK
• Kim YS
• Roh TS
• Yun IS

• KMID: 2417798
• DOI: http://doi.org/10.7181/acfs.2018.01704

Abstract

Parry-Romberg syndrome is a rare neurocutaneous syndrome characterized by progressive shrinkage and degeneration of the tissues usually on only one side of the face. It is usually difficult to restore the facial contour due to skin tightness. In this case report, we report a forehead reconstruction with custom-made three-dimensional (3D) titanium implant of a Parry-Romberg syndrome patient who was treated with multiple fat grafts but had limited effect. A 36-year-old man presented with hemifacial atrophy. The disease progressed from 5 to 16 years old. The patient had alopecia on frontal scalp and received a surgery using tissue expander. The alopecia lesion was covered by expanded scalp flap done 22 years ago. Also, he was treated with fat grafts on depressed forehead 17 years ago. However, it did not work sufficiently, and there was noted depressed forehead. We planned to make 3D titanium implant to cover the depressed area (from the superior orbital rim to the vertex). During the operation, we confirmed that the custom-made 3D implant accurately fit for the depressed area without any dead spaces. Previously depressed forehead and glabella were elevated, and the forehead contour was improved cosmetically. A custom-made 3D titanium implant is widely used for skull reconstruction and bring good results. In our case, the depressed forehead of a Parry-Romberg syndrome patient was improved by a 3D titanium implant.

Keyword

Titanium; Facial hemiatrophy; Parry-Romberg disease

MeSH Terms

Adult
Alopecia
Facial Hemiatrophy*
Forehead*
Humans
Neurocutaneous Syndromes
Orbit
Scalp
Skin
Skull
Tissue Expansion Devices
Titanium*
Transplants
Titanium