J Korean Soc Radiol.  2018 Aug;79(2):97-100. 10.3348/jksr.2018.79.2.97.

CT Findings of Quadricuspid Pulmonary Valve with Pulmonary Artery Aneurysm

Affiliations
  • 1Department of Radiology, Korea University Guro Hospital, Seoul, Korea. yhwanseok@naver.com

Abstract

Quadricuspid pulmonary valve (QPV) with pulmonary artery aneurysm is an uncommon condition. QPV is typically clinically silent, so it is often diagnosed after death. However, recent advancements in imaging modalities, such as computed tomography (CT), have allowed more frequent incidental diagnosis of QPV in living adults. We report a case of QPV with pulmonary artery aneurysm in an asymptomatic adult; the condition was detected by CT aortography but was not discernible in echocardiography. Following the case presentation, we review the prior related literature.


MeSH Terms

Adult
Aneurysm*
Aortography
Congenital Abnormalities
Diagnosis
Echocardiography
Humans
Pulmonary Artery*
Pulmonary Valve*
Tomography, X-Ray Computed

Figure

  • Fig. 1 These figures show QPV with pulmonary artery aneurysm. A. Chest radiography shows bulging opacity in the left hilum, probably due to prominent vascular shadow B, C. Double oblique reconstruction CT image shows QPV (arrow, B) and normal tricuspid AV (arrowhead, C). D. Axial CT image shows dilated pulmonary artery, suggesting pulmonary artery aneurysm. AV = aortic valve, QPV = quadricuspid pulmonary valve

  • Fig. 2 This figure shows embryogenesis of QPV and normal tricuspid AV. Abnormal mesenchymal proliferation is the first step leading to QPV. AV = aortic valve, QPV = quadricuspid pulmonary valve


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