J Korean Soc Radiol.  2018 May;78(5):358-362. 10.3348/jksr.2018.78.5.358.

A Rare Case of Zinner's Syndrome with Ectopic Prostate and Triorchidism

• Ko A
• Lee ES
• Park HJ
• Lee JB
• Choi BI

• KMID: 2410727
• DOI: http://doi.org/10.3348/jksr.2018.78.5.358

Abstract

Zinner's syndrome is a rare congenital abnormality of the mesonephric duct. Unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction are the triad of maldevelopment of the mesonephric duct which comprises Zinner's syndrome. It is an extremely rare case, in that approximately 100 cases only have been reported worldwide. We discovered a rare developmental anomaly with other mesonephric duct-associated abnormalities, Zinner's syndrome with a presumed ectopic prostate and triorchidism and do report here.

MeSH Terms

Congenital Abnormalities
Ejaculatory Ducts
Male
Prostate*
Seminal Vesicles
Tomography, X-Ray Computed
Ultrasonography
Urogenital System
Wolffian Ducts

Figure

• 

  Fig. 1 A 23-year-old male presented with history of urinary retention and dysuria. A. Computed tomography images show homogeneous enhancement in the left kidney without perfusion defects in nephrographic phase and good excretory function. A dilated cystic tubular structure (asterisk) is found in the right seminal vesicle. In the bladder, a bi-lobed filling defect (arrow) is depicted in the trigone on excretory phase. B. A bi-lobed submucosal mass (asterisk) with intact overlying bladder mucosa (line, M) is seen on transrectal ultrasonography and shows similar echogeniticy with the normal prostate (P) without abnormal vascualrity. The cystic and tubular lesion (SV) in the right seminal vesicle is also seen. C. Normal right epididymal head (E) and testis (T) with an additional smaller and round mass (asterisk) which has similar echogenicity with normal testis at the inferior aspect of the normal testis, presumed polyorchidism.

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