Korean J Thorac Cardiovasc Surg.  2018 Feb;51(1):64-68. 10.5090/kjtcs.2018.51.1.64.

Hughes-Stovin Syndrome as an Outcome of Behçet Disease or as a Different Entity

• Demirkan S
• Gültekin

• KMID: 2409716
• DOI: http://doi.org/10.5090/kjtcs.2018.51.1.64

Abstract

Hughes-Stovin syndrome is a rare disorder of unknown etiology. Although the association between multiple pulmonary artery aneurysms and venous thrombosis of the lower limbs was reported by Beattie and Hall in 1911, it was not until 1962 that the eponym "Hughes-Stovin syndrome" was formally introduced in the medical literature. We describe 2 patients with Hughes-Stovin syndrome who presented with pulmonary artery aneurysm, thrombophlebitis, hemoptysis, and oral ulcers, review the manifestations of the disease, and compare its similarities with and differences from Behçet disease.

Keyword

Hughes-Stovin syndrome; Behçet disease; Pulmonary artery aneurysms; Thrombosis; Oral ulcer

MeSH Terms

Aneurysm
Behcet Syndrome*
Eponyms
Hemoptysis
Humans
Lower Extremity
Oral Ulcer
Pulmonary Artery
Thrombophlebitis
Thrombosis
Venous Thrombosis