J Korean Assoc Pediatr Surg.  2017 Dec;23(2):52-54. 10.13029/jkaps.2017.23.2.52.

Unusual Giant Arteriovenous Malformation in Jejunum: A Case Report

• Kim D
• Goo J

• KMID: 2398577
• DOI: http://doi.org/10.13029/jkaps.2017.23.2.52

Abstract

Polypoid or tumorous arteriovenous malformation (AVM) of small intestine is rare and can be misdiagnosed as other tumorous conditions. We experienced a rare case of giant jejunal AVM in a 15-year-old boy, who complained of intense abdominal pain. Ultrasonography and contrast-enhanced CT revealed a 13.5-cm-sized multiseptated cystic mass arising in small intestine, which was mimicking submucosal tumor. It was successfully treated by surgical resection. The specimen showed a multilobulated outbulging submucosal mass in jejunum. Histopathologic evalulation confirmed AVM located in the submucosa, muscularis propria and subserosa. This case is the largest AVM of small intestine among which has ever been reported.

Keyword

Arteriovenous malformations; Jejunum; Submucosa; Tumor

MeSH Terms

Abdominal Pain
Adolescent
Arteriovenous Malformations*
Humans
Intestine, Small
Jejunum*
Male
Tomography, X-Ray Computed
Ultrasonography

Figure

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  Fig. 1 Ultrasonographic finding. Ultrasonography revealed a multiseptated cystic mass with internal hemorrhage in pelvic cavity.

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  Fig. 2 Surgical specimen and microscopic findings. (A) The surgical specimen showed a well demarcated submucosal mass with multicystic appearance. The cystic spaces were filled with blood clots. (B) The histologic examination showed intact mucosal cover and various sized abnormal vessels in the submucosa. Some vessels had thin collagenous wall of veins and others had thick muscular wall of arteries (H&E, ×40).

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