Ann Clin Neurophysiol.  2017 Jan;19(1):68-70. 10.14253/acn.2017.19.1.68.

Flail arm syndrome with several issues related to the diagnostic process

• Kim JY
• Park YK
• Yoon B
• Lee KO
• Kim YD
• Na SJ

• KMID: 2367999
• DOI: http://doi.org/10.14253/acn.2017.19.1.68

Abstract

Flail arm syndrome (FAS), known as one of the atypical amyotrophic lateral sclerosis (ALS) variants, has a similar clinical course and pathologic findings as ALS. Therefore it is difficult to differentiate between ALS and FAS at a glance. There are few reports involving individual analysis of FAS patients to date. The findings of polysomnography (PSG) in patient with FAS are not well known. We report a male FAS patient with review of literatures and several issues related to the diagnostic process.

Keyword

Flail arm syndrome; Amyotrophic lateral sclerosis; Upper motor neuron sign

MeSH Terms

Amyotrophic Lateral Sclerosis
Arm*
Humans
Male
Polysomnography

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