Ann Dermatol.  1996 Oct;8(4):260-264. 10.5021/ad.1996.8.4.260.

A Case of Epidermal Nevus Syndrome Associated with Urogenital Abnormalities

• Ha SJ
• Lee SC
• Kim SY
• Kim CW

• KMID: 2360446
• DOI: http://doi.org/10.5021/ad.1996.8.4.260

Abstract

The epidermal nevus syndrome is a disorder characterized by epidermal nevi and associated neurologic, skeletal, and other abnormalities. A 15-year-old female patient presented with extensive, bilateral systematized, verrucous plaques, involving the face, trunk, both extremities, and anogenital area. The onset of the lesions were at the age of 2 months. Abdominal CT showed the absence of the left kidney, teratoma of the right ovary and left ovarian cyst. This is a case of epidermal nevus syndrome, which was composed of extensive epidermal nevi, congenital solitary kidney, left ovarian cyst and right ovarian teratoma.

Keyword

Epidermal nevus syndrome; Ovarian cyst and teratoma; Solitary kidney

MeSH Terms

Adolescent
Extremities
Female
Humans
Kidney
Nevus*
Ovarian Cysts
Ovary
Teratoma
Tomography, X-Ray Computed
Urogenital Abnormalities*