Ann Dermatol.  1998 Jul;10(3):167-171. 10.5021/ad.1998.10.3.167.

An Unusual Case of Churg-Strauss Syndrome

• Chang SE
• Cheong JK
• Choi JH
• Sung KJ
• Moon KC
• Koh JK

• KMID: 2359784
• DOI: http://doi.org/10.5021/ad.1998.10.3.167

Abstract

Churg-Strauss syndrome (CSS) is a very rare disease which combines the features of asthma, hypereosinophilia, multisystem necrotizing vasculitis and extravascular granuolma. To our knolwedge, there have been four reports in Korean journals, but none in dermatology journals. We report a 37-year-old male who had allergic rhinitis, pansinusitis, a history of atopic dermatitis, multiple prurigo-nodularis like skin lesions, non-fixed interstitial lung in-filtration, hypereosinophilia and subclinical asthma. Clinical and histopathological features of his skin lesions were nonspecific where perivascular lymphocytic infiltration and mild lymphocytic vasculitis were shown. The presence of a pituitary mass and proximal myopathy as op-posed to peripheral neuropathy have not been reported in previous reports of CSS. However, other features of our patient met the criteria of CSS.

Keyword

Churg-Strauss syndrome; Subclinical asthma

MeSH Terms

Adult
Asthma
Churg-Strauss Syndrome*
Dermatitis, Atopic
Dermatology
Humans
Lung
Male
Muscular Diseases
Peripheral Nervous System Diseases
Rare Diseases
Rhinitis, Allergic
Skin
Vasculitis