J Korean Ophthalmol Soc.  2016 Nov;57(11):1777-1780. 10.3341/jkos.2016.57.11.1777.

Dermatofibrosarcoma in the Orbit: A Case Report

• Lee DK
• Kim GE
• Choi W
• Yoon KC

• KMID: 2357735
• DOI: http://doi.org/10.3341/jkos.2016.57.11.1777

Abstract

PURPOSE
Dermatofibrosarcoma in the orbit is a rare malignant neoplasm. We report an extremely rare case of primary dermatofibrosarcoma in the orbit.
CASE SUMMARY
A 66-year-old male presented with a slowly progressing periorbital mass on his left upper eyelid which developed 3 weeks earlier. On physical examinations, a palpable firm mass under the skin was observed at the superomedial aspect of the left upper eyelid. However, there was no surface nodule or demarcated line on the eyelid. An approximately 1.2 × 1 × 1 cm sized well defined and clearly demancated mass was observed on orbital computed tomography. Excisional biopsy was performed under local anesthesia and pathological examination revealed dermatofibrosarcoma. There was no metabolic evidence of regional or distant metastasis based on positron emission tomography-computed tomography. Nine months after surgical excision there was no evidence of local recurrence.
CONCLUSIONS
This is the first report in South Korea of dermatofibrosarcoma in the orbit. Dermatofibrosarcoma should be considered following differential diagnosis of a periorbital mass.

Keyword

Dermatofibrosarcoma; Orbital mass

MeSH Terms

Aged
Anesthesia, Local
Biopsy
Dermatofibrosarcoma*
Diagnosis, Differential
Electrons
Eyelids
Humans
Korea
Male
Neoplasm Metastasis
Orbit*
Physical Examination
Recurrence
Skin

Figure

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  Figure 1. Clinical photos and Orbital computed tomography. Photograph of (A) 66-year-old man with a palpable firm mass under the skin at the superomedial aspect of the left upper eyelid. (B) Orbital computed tomography showed 1.2 × 1 × 1 cm sized well demarcated enhancing mass. (C) The orbital mass immediate after surgical excision. (D) The 9 months after operation showed no evidence of recurrence.

• 

  Figure 2. Photographs of Histopathology. (A) Photograph of dermatofibrosarcoma by hematoxylin-eosin (×200). The tumor is composed of spindle cells with a fascicular arrangement. A mitotic activity is also shown. (B) Immunohistochemical staining shows CD34 positive cells (×200).

Reference

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