J Korean Soc Radiol.  2010 Oct;63(4):323-327.

Dyshormonogenic Goiter within Ectopic Thyroid: A Case Report

• Lee WH
• Han JK
• Kim YT
• Jou SS
• Kim SW
• Kim SY
• Cho HD

Abstract

A dyshormonogenetic goiter is a congenital hyperplasia of the thyroid parenchyma caused by a defect in the noraml hormongenetic pathway. Here, we report on a case involving the simultaneous occurrence of a thyroid and an ectopic thyroid dyshormonogenetic goiter. We describe the ultrasound and CT findings along with a brief literature review.

MeSH Terms

Congenital Hypothyroidism
Goiter
Hyperplasia
Thyroid Dysgenesis
Thyroid Gland
Thyroid Neoplasms

Figure

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  Fig. 1 Neck CT and ultrasonography of goiter and left neck mass in 45-year-old female. A. Axial image of non-contrast enhanced CT shows low attenuated thyroid gland and left neck mass with high attenuated portions (arrow) and small calcifications. B. Axial image of contrast enhanced CT shows heterogenous enhancements in thyroid gland and left neck mass with non-enhancing foci (arrow). C. Ultrasonographic finding shows heterogenous isoechoic mass in left supraclavicular area. D. Ultrasonographic finding shows a nodular calcification in left thyroid gland.

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  Fig. 2 Microscopic histology of goiter and left neck mass in 45-year-old female. A. A photomicrograph of goiter shows multiple hyperplastic nodules with fibrotic tissue (black arrow) and calcification (H & E, ×100). B. A photomicrograph of goiter shows complex microfollicles with atypical nodules in the fibrosis tissue between hyperplastic nodules (H & E, ×400). C. A photomicrograph of neck mass shows normal thyroid tissue and multiple hyperplastic nodules with fibrotic tissue (H & E, ×100). D. A photomicrograph of neck mass shows similar microscopic findings with goiter (H & E, ×400).

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