J Korean Neurol Assoc.
1998 Apr;16(2):241-244.
A Case of Porphyria with reversible MRI findings
- Affiliations
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- 1Dept. of Neurology, Ulsan University, College of Medicine, Asan Medical Center.
Abstract
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The porphyrias are inherited or acquired disorders of specific enzymes in the heme biosynthetic pathway. Porphyrias have diverse neurologic manifestations with unknown mechanism. Some authors have proposed ischemic vasculopathy as a cause of neurologic deficits, which was supported by reversible MRI lesions in porphyrias. We report a rare case with reversible MRI findings in porphyria. A 27-year-old woman was presented with seizures and hallucinations. MRI revealed multiple lesions of both hemispheres. After treatment, MRI lesions showed marked resolution of signal abnormalities.