J Korean Ophthalmol Soc.  1989 Jun;30(3):437-742.

A Case of Orbital Rhabdomyoma Removed by Subtotal Orbital Exenteration with Preservation of Conjunctiva, Cornea and Sclera

• Hong JW
• Joo HS
• Lee TS

Abstract

Orbital rhabdomyoma is an exceedingly rare, benign, slow growing tumor of mature myofibers. The authors experienced a case of orbital rhabdomyoma in three-year old female who had limitation of eyeball movement with marked proptosis of the left eye. The subtotal orbital exenteration with preservation of lid, conjunctiva, cornea, and sclera through lateral orbitotomy was performed. The removed tumor was consisted of many irregularly shaped fragments of grayish tan soft tissue, me as uring 0.7 X 1.8 X 1.0 cm in size. Pathologically it was proved as orbital rhabdomoma as seen in adult. Postoperatively the conjunctival sac was well preserved and artificial eye could be successfully fitted.

Keyword

rhabdomyoma; subtotal orbital exenteration; conjunctival sac; artificial eye

MeSH Terms

Adult
Conjunctiva*
Cornea*
Exophthalmos
Eye, Artificial
Female
Humans
Orbit*
Rhabdomyoma*
Sclera*
Triacetoneamine-N-Oxyl
Triacetoneamine-N-Oxyl