J Korean Orthop Assoc.  2013 Aug;48(4):319-323.

Sprengel Deformity with Bilateral Huge Omovertebra

• Yoon GW
• Chung SH

Abstract

Sprengel's deformity is characterized by the congenital migration of the scapula superiorly in relation to the thoracic cage. Other congenital anomalies, such as Klippel-Feil syndrome, may occur in combination with Sprengel's deformity. We report on a case of Sprengel's deformity with a huge bilateral omovertebrae, which was combined with the clinical features of Klippel-Feil syndrome, including cervical fusion, short neck, low posterior hairline, and limitation of neck motion. However, no other deformities or functional defects were observed.

Keyword

Sprengel deformity; Klippel-Feil syndrome

MeSH Terms

Congenital Abnormalities
Klippel-Feil Syndrome
Neck
Scapula
Shoulder Joint
Congenital Abnormalities
Scapula
Shoulder Joint