J Korean Pediatr Cardiol Soc.  2006 Mar;10(1):45-49.

A Case of Congenital Unilateral Pulmonary Vein Atresia

• Choi EK
• Song MS
• Kim YW
• Kim CH

Abstract

Congenital unilateral pulmonary vein atresia is a very rare cardiac malformation. In this case, the patient was brought to the hospital for recurrent upper respiratory infection without exertional dyspnea or hemoptysis, and cardiac murmurs were heard on physical examination. The volume of affected lung was lost on simple chest x-ray. Lung perfusion scan revealed no visualization of affected lung. Cardiac catheterization revealed mild pulmonary artery hypertension. Pulmonary angiography showed a small right pulmonary artery, stasis of contrast material and venous phase revealed nonvisualization of draining right pulmonary veins. In this case, the patient did not undergo any surgical treatment for no symptoms other than recurrent upper respiratory infection were reported. We report a case of congenital right pulmonary vein atresia.

Keyword

Congenital pulmonary vein atresia; Unilateral

MeSH Terms

Angiography
Cardiac Catheterization
Cardiac Catheters
Dyspnea
Heart Murmurs
Hemoptysis
Humans
Hypertension
Lung
Perfusion
Physical Examination
Pulmonary Artery
Pulmonary Veins*
Thorax