J Korean Child Neurol Soc.  2007 Nov;15(2):179-184.

Moyamoya Disease in Children and Adolescents

Affiliations
  • 1Department of Pediatrics, School of Medicine, Inje University, Busan, Korea. htg6700@chollian.net

Abstract

PURPOSE: Moyamoya disease is a chronic cerebrovascular illness characterized by bilateral stenoses or occlusions of the arteries around the circle of Willis with prominent collateral circulation. We studied 36 children and adolescents with Moyamoya disease to evaluate the clinical features and outcomes.
METHODS
Records were reviewed of 36 pediatric patients admitted at the Busan Paik Hospital for Moyamoya disease between January 2000 and July 2007. The clinical records were reviewed in terms of the patient profiles, imaging findings, surgical techniques, and pathologic findings.
RESULTS
Overall clinical features, responses to treatment and outcome were nearly same as those of other previous reports in Korea as well as the other countries. The mean age of onset was 8 years and 5 months and the ratio of male to female was 1:1.2. Ischemia was more often than infarction(5.6: 1). Half of the patients had conservative therapy and 17 cases(47%) were treated with EDAS.
CONCLUSION
The clinical features of childhood Moyamoya disease are similar to the result from other studies in Korea.

Keyword

Childhood Moyamoya disease; Clinical features

MeSH Terms

Adolescent*
Age of Onset
Arteries
Busan
Child*
Circle of Willis
Collateral Circulation
Constriction, Pathologic
Female
Humans
Ischemia
Korea
Male
Moyamoya Disease*
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