J Korean Soc Radiol.  2013 Dec;69(6):461-464.

Lipomatosis of the Jejunum with Volvulus: A Case Report

• Kang KA
• Bae KE
• Kim SH
• Kang MJ
• Lee J
• Lee HB
• Kim JH
• Jeong MJ
• Kim HJ

Abstract

Intestinal lipomatosis is an extremely rare disease that is characterized by numerous lipomas of the intestine. This condition is usually asymptomatic, but clinical presentation is determined by intussusceptions, volvulus, or ulceration. We report a case of intestinal lipomatosis of the jejunum with volvulus and describe the characteristic computed tomography findings that were used to make a preoperative diagnosis.

MeSH Terms

Diagnosis
Intestinal Volvulus*
Intestine, Small
Intestines
Intussusception
Jejunum*
Lipoma
Lipomatosis*
Rare Diseases
Ulcer

Figure

• 

  Fig. 1 A 50-year-old man presented with severe acute abdominal pain. A. Conventional abdominal radiography shows dilated small bowel loops with multiple air-fluid levels (arrows) in the left abdomen. B, C. Contrast enhanced axial CT scan demonstrates small bowel volvulus, SMV (long arrow) on the left of SMA (short arrow) with a whirl-like pattern, and a dilated proximal small bowel (open arrow). D-F. Coronal reformatted (D) and axial (E, F) images show multiple homogeneous fat attenuating masses within the small bowel in right lower abdomen (arrows). Note the small air-containing outpouchings in the wall of the affected small bowel (open arrows), which represent diverticula. G. Gross appearance of the resected small intestine shows multiple intraluminal fatty polypoid masses (more than one hundred in number), measuring up to 6 cm in dimension. H. Photomicrography shows a submucosal mass composed of mature adipocytes with intact mucosa (H&E, × 40). Note.-SMA = superior mesenteric artery, SMV = superior mesenteric vein

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