Tuberc Respir Dis.  2001 Apr;50(4):493-498. 10.4046/trd.2001.50.4.493.

A Case of Systemic Sclerosis Sine Scleroderma Presenting as Pulmonary Interstitial Fibrosis

• Kwak JH
• Choi WI
• Lee SH
• Seo CG
• Kim KC
• Kim MS
• Kwon KY
• Suh SJ
• Park CK
• Jeon YJ

• KMID: 2318329
• DOI: http://doi.org/10.4046/trd.2001.50.4.493

Abstract

Lung involvement in systemic sclerosis(SSC) is common but usually occurs late in the course. Skin changes usually occur before the pulmonary findings. In this report, a patient who developed pulmonary interstitial fibrosis without skin changes is presented. A diagnosis of SSC lung involvement was made histologically. The a nti-scl-70 antibody test was positive. Esophageal manometry revealed a lower amplitude in the lower two-third of the esophagus and pressure in the lower esophageal sphincter. Here we report a case of wystemic sclerosis sine scleroderma presenting as pulmonary interstitial fibrosis with a review of the relevant literatures.

Keyword

Systemic sclerosis sine scleroderma; Pulmonary interstitial fibrosis

MeSH Terms

Diagnosis
Esophageal Sphincter, Lower
Esophagus
Fibrosis*
Humans
Lung
Manometry
Scleroderma, Systemic*
Sclerosis
Skin