Obstet Gynecol Sci.  2014 Nov;57(6):549-552. 10.5468/ogs.2014.57.6.549.

Unusual bilateral vulvar liposarcoma

• Kwak JH
• Shin SM
• Kim JW
• Lee NW

• KMID: 2314026
• DOI: http://doi.org/10.5468/ogs.2014.57.6.549

Abstract

Liposarcoma of vulva is a rare malignant tumor. Only fifteen cases of vulvar liposarcoma have been reported in English literature. Because of extreme rarity of vulvar liposarcoma, it is initially misdiagnosed as benign tumor such as lipoma. This paper aims to present a unique case of liposarcoma of bilateral vulvae with a review of the literature of previously reported cases.

Keyword

Lipoma; Liposarcoma; Radiotherapy; Vulva

MeSH Terms

Lipoma
Liposarcoma*
Radiotherapy
Vulva

Figure

• 

  Fig. 1 Radiologic image, gross photo and histopathologic finding of vulvar liposarcoma. (A) Magnetic resonance imaging T1-weighted enhanced image revealed bilateral vulvar masses that show similar signal intensity as surrounding fat tissue without definite enhancement portion. (B) Specimen consists of many irregular adipose tissues. (C) Histologic sections of lipomatous tumor show variable sized adipocytes with atypical myxoid stromal cell (×100).

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