Korean Circ J.  2010 Feb;40(2):86-89. 10.4070/kcj.2010.40.2.86.

Primary Cardiac Angiosarcoma Presenting With Cardiac Tamponade

Affiliations
  • 1Division of Cardiology, Department of Internal Medicine, Sanggye Paik Hospital, Inje University College of Medicine, Seoul, Korea. ysbyun@paik.ac.kr
  • 2Department of Thoracic and Cardiovascular Surgery, Sanggye Paik Hospital, Inje University College of Medicine, Seoul, Korea.
  • 3Department of Pathology, Sanggye Paik Hospital, Inje University College of Medicine, Seoul, Korea.

Abstract

Primary cardiac angiosarcoma is a very rare disease with a poor prognosis. We report a case of a patient with a primary cardiac angiosarcoma who presented with cardiac tamponade; the angiosarcoma was successfully resected surgically.

Keyword

Cardiac tumor; Angiosarcoma; Hemopericardium

MeSH Terms

Cardiac Tamponade
Heart Neoplasms
Hemangiosarcoma
Humans
Pericardial Effusion
Prognosis
Rare Diseases

Figure

  • Fig. 1 Round, increased cardiac silhouette and right costophrenic angle blunting on chest radiography.

  • Fig. 2 Chest CT (A) and transthoracic echocardiography (B) shows a large and inhomogeneous, enhancing mass in the right atrium (arrow) and a massive amount of pericardial and right pleural effusion.

  • Fig. 3 Transesophageal echocardiography shows a primary cardiac mass without involvement of the inferior and superior vena cava. IVC: inferior vena cava, SVC: superior vena cava, RA: right atrium, LA: left atrium.

  • Fig. 4 A: a resected protruding mass (6.8×6.5×2.5 cm) into the right atrial chamber is present at the atrial wall. B: the cut surface is diffusely hemorrhagic with a gray-white fleshy solid portion. C: the tumor is composed of oval-to-spindle cells with intracytoplasmic red blood cells. There are frequent mitoses (> 10/10 HPF). D: the tumor cells are positive for CD34 immunohistochemical staining.


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