Korean Circ J.  2011 May;41(5):272-275. 10.4070/kcj.2011.41.5.272.

Isolated Double-Chambered Right Ventricle in a Young Adult

• Park JG
• Ryu HJ
• Jung YS
• Kim KJ
• Lee BR
• Jung BC
• Kang H

• KMID: 2297935
• DOI: http://doi.org/10.4070/kcj.2011.41.5.272

Abstract

Double-chambered right ventricle (DCRV) is a rare congenital heart disorder in which the right ventricle is divided by an anomalous muscle bundle into a high pressure inlet portion and a low pressure outlet portion. We report a case of isolated DCRV without symptoms in adulthood, diagnosed through echocardiography, cardiac catheterization and cardiac magnetic resonance imaging.

Keyword

Heart defeets, congenital; Cardiac catheterization; Echocardiography; Magnetic resonance imaging

MeSH Terms

Bays
Cardiac Catheterization
Cardiac Catheters
Echocardiography
Heart
Heart Ventricles
Humans
Magnetic Resonance Imaging
Muscles
Young Adult

Figure

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  Fig. 1 Double-chambered right ventricle demonstrated by transthrorasic echocardiography. A: two-dimensional echocardiography showing a stenotic mid-right ventricle with an anomalous muscle bundle (arrow). B: turbulent Doppler color flow with mosaic pattern. C: continuous-wave Doppler showing tricuspid regurgitation between the right atrium and right ventricle and indicating the flow acceleration and pressure gradient. RV: right ventricle, LV: left ventricle, RA: right atrium.

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  Fig. 2 Transesophageal echocardiography showing anomalous muscular bundles (arrow) dividing the right ventricle into two parts. RV: right ventricle, LV: left ventricle, RA: right atrium, LA: right atrium.

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  Fig. 3 Two-dimensional cine MRI showing anomalous muscle bundle (arrow). RV: right ventricle, RA: right atrium.

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  Fig. 4 Right ventriculogram demonstrating a severe hypertrophied muscle bundle (arrow). RV: right ventricle, RA: right atrium, PA: pulmonary artery.

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  Fig. 5 Cardiac catheterization showing systolic pressure gradient between RVIT and RVOT. RVIT: right ventricular inlet tract, RVOT: right ventricular outlet tract.

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