Korean J Urol.  2006 Mar;47(3):334-340. 10.4111/kju.2006.47.3.334.

Initial Experiences of Complete Primary Exstrophy Repair in Cloacal and Bladder Exstrophy

• Kang T
• Yoo CH
• Kim KS

• KMID: 2294184
• DOI: http://doi.org/10.4111/kju.2006.47.3.334

Abstract

We report here the short-term results of 3 cases of cloacal and bladder exstrophy that underwent complete primary exstrophy repair. One case was diagnosed as bladder exstrophy and the others were diagnosed as cloacal exstrophy. Complete primary exstrophy repair for all 3 cases was carried out within 24 hours after birth. There was no wound dehiscence within the follow-up period of 12 months. The complete primary exstrophy repair with positioning the bladder neck and urethra in the deep pelvic cavity achieves a satisfactory short-term result.

Keyword

Bladder exstrophy; Cloaca; Reconstructive surgical procedures

MeSH Terms

Bladder Exstrophy*
Cloaca
Follow-Up Studies
Neck
Parturition
Reconstructive Surgical Procedures
Urethra
Urinary Bladder*
Wounds and Injuries

Figure

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  Fig. 1 The preoperative findings and illustration of case 1.

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  Fig. 2 Intraoperative procedures of complete primary exstrophy repair. (A) Dissection of the exstrophied bladder from the abdominal wall. (B) Primary repair of the bladder and urethra. (C) Proper positioning of the bladder neck and the proximal urethra within the pelvic diaphragm and closure of the symphysis pubis. (D) Immediate postoperative findings.

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  Fig. 3 The preoperative findings and illustration of case 2.

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  Fig. 4 Intraoperative procedures. (A) Dissection of exstrophied cloaca from the abdominal wall. (B) Deep positioning of the bladder neck and the proximal urethra within the pelvic diaphragm and closure of the symphysis pubis. (C) The postoperative photograph at 6 months.

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  Fig. 5 The preoperative findings and illustration of case 3.

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  Fig. 6 Immediate postoperative findings.

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