Korean J Urol.
2002 Nov;43(11):987-990.
Epithelioid Angiomyolipoma of the Kidney with Distant Metastasis
- Affiliations
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- 1Department of Urology, Hanyang University College of Medicine, Seoul, Korea. harabugi@hanyang.ac.kr
Abstract
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An epithelioid angiomyolipoma is an uncommon clinicopathological variant of an angiomyolipoma. A 25-year-old man presented with a huge right renal tumor and underwent a radical nephrectomy. The pathological diagnosis was an epithelioid angiomyolipoma, which showed a positive reaction to the HMB-45 monoclonal antibody and negative to epithelial cell markers. A year later, multiple metastases developed to the liver, lungs and bones. A hepatic lobectomy was performed, and a metastatic epithelioid angiomyolipoma, from the original renal tumor, was pathologically confirmed. The case is presented with a review of the literature.