Korean J Urol.
1998 Nov;39(11):1158-1160.
Persistent Mullerian Duct Syndrome in a Boy with Transverse Testicular Ectopia: a Case Report
- Affiliations
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- 1Department of Urology, Catholic University of Taegu-Hyosung, College of Medicine, Taegu, Korea.
Abstract
- Persistent mullerian duct syndrome is characterized by the presence of mullerian structures in male subiects with normal penile and scrotal development. A deficiency of activity of a mullerian inhibiting substance during gestation is believed to be responsible for this syndrome. To date approximately 150 cases of persistent mullerian duct syndrome have been reported and the syndrome of transverse testicular ectopia with persistent mullerian duct structures is much rarer. In Korea, this is the fourth case to be reported. We report a case of persistent mullerian duct syndrome with transverse testicular ectopia in a 7 month-old-boy. Both testes were in the right side of scrotum but no epididymises were found there, which resulted in the disruption of normal relationship between the was and testis. Regarding there was no fertility, mullerian duct structures were removed.
