Korean J Thorac Cardiovasc Surg.  2000 Oct;33(10):823-826.

Primary Intimal Sarcoma Originating from Pulmonary Valve

• Lee JW
• Ryu SW
• Choo SJ
• Song H
• Song MG

Abstract

Primary intimal sarcoma of the pulmonary artery is a rare disease and there has been no report of any case originating from the pulmonary valve. Recently we experienced a 62 year-old female patient who had a primary intimal sarcoma of the pulmonary valve with distal metastasis. She was brought to medical attention due to exertional dyspnea facial edema productive coughing and general weakness for 1 month. Chest CT and echocardi-ography suggest an acute pulmonary thromboembolism or tumor. Exploration showed a large polypoid mass arising from the pulmonary leaflets and multiple masses on distal pulmonary arteries. We replaced the pulmonary valve and reconstructed the pulmonary artery. She received radiotherapy 1 month postoperatively and now 4 months after surgery she has begun receiving chemotherapy.

MeSH Terms

Cough
Drug Therapy
Dyspnea
Edema
Female
Humans
Middle Aged
Neoplasm Metastasis
Pulmonary Artery
Pulmonary Embolism
Pulmonary Valve*
Radiotherapy
Rare Diseases
Sarcoma*
Tomography, X-Ray Computed