Korean J Thorac Cardiovasc Surg.  1997 Feb;30(2):231-235.

Congenital Cystic Adenomatoid Malformation Associated with Pectus Excavatum: 1 case report

• Ahn BH
• Moon HS
• Na KJ
• Kim SH

Abstract

Congenital cystic adenomatoid malformation of the lung is a rare pulmonary malformation, Although it is one of the most common congenital anomalies which cause acute respiratory distress in the newborn infants, characterized by marked proliferation of terminal respiratory structures. We have experienced an unusual case of congenital cystic adenomatoid malformation associated with pectus excavatum. The patient was 3-year-old female who suffered from cough and high fever for 20 days, and antibiotic therapy was given in other hospital before transfer to our hospital. The findings on chest X-ray, chest CT, aortogram, and selective bronchial arteriogram showed cystic lesions in the right upper and middle lobe accompanied but severe pectus excavatum. Right bilobectomy for pulmonary lesion and costosternal elevation for pectus excavatum was performed simultaneously with successful result. The postoperative course was uneventful and the patient was discharged on the twentieth postoperative day.

Keyword

congenital cystic adenomatoid malformation; pectus excavatum

MeSH Terms

Child, Preschool
Cough
Cystic Adenomatoid Malformation of Lung, Congenital*
Female
Fever
Funnel Chest*
Humans
Infant, Newborn
Lung
Thorax
Tomography, X-Ray Computed