Korean J Otolaryngol-Head Neck Surg.  2006 Apr;49(4):439-442.

Decompression of Internal Auditory Canal via Middle Fossa Approach in Neurofibromatosis Type II with Only Hearing Ear

Affiliations
  • 1Department of Otorhinolaryngology, Yonsei University College of Medicine, Seoul, Korea. hokilee@yumc.yonsei.ac.kr

Abstract

Neurofibromatosis type II (NF2) is a genetic disease and is transmitted as an autosomal dominant trait. NF2 is characterized by bilateral acoustic neuroma with multiple tumors of central nervous system. Progressive hearing loss is a significant problem in patients with NF2, and hearing preservation is an important factor for choice of treatment plan, especially in a NF2 patient with only one hearing ear. We report an experience of preservation of hearing in a NF2 patient with only one hearing ear through decompression of the internal auditory canal via middle cranial fossa approach.

Keyword

Neurofibromatosis 2; Acoustic neuroma; Decompression surgical

MeSH Terms

Central Nervous System
Cranial Fossa, Middle
Decompression*
Ear*
Hearing Loss
Hearing*
Humans
Neurofibromatoses*
Neurofibromatosis 2*
Neuroma, Acoustic
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