Korean J Pathol.  2000 May;34(5):389-392.

Multiple Plexiform Schwannomas Associated with Neurofibromatosis Type 2: A case report

Affiliations
  • 1Departments of Pathology, Chonbuk National University Medical School, Chonju 561-180, Korea.
  • 2Departments of Ophthalmology, Chonbuk National University Medical School, Chonju 561-180, Korea.

Abstract

Plexiform schwannoma is a rare benign tumor arising from the peripheral nerve sheath and characterized by a multinodular and plexiform growth pattern. This tumor usually arises sporadically. In rare cases, plexiform schwannomas have been associated with neurofibromatosis type 2. Plexiform schwannoma should be differentiated from plexiform neurofibroma, because the latter is pathognomonic tumor of neurofibromatosis type 1 and has a potential of malignant transformation. We report a case of multiple plexiform schwannomas associated with bilateral acoustic neuromas and meningioma.

Keyword

Plexiform schwannoma; Neurofibromatosis type 2

MeSH Terms

Meningioma
Neurilemmoma*
Neurofibroma, Plexiform
Neurofibromatoses*
Neurofibromatosis 1
Neurofibromatosis 2*
Neuroma, Acoustic
Peripheral Nerves
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