Korean J Otolaryngol-Head Neck Surg.  1998 Dec;41(12):1598-1603.

Congenital Aural Atresia Associated with Cholesteatoma

Affiliations
  • 1Department of Otorhinolaryngology, Seoul National University College of Medicine, Seoul, Korea.

Abstract

Congenital aural atresia (CAA) with variable degrees of microtia are combined with many other otologic or facial anomalies. Among them, cholesteatoma developed behind atretic plate is rarely reported. Since Von Luders had first reported about this condition at 1912, several authors had described CAA associated with cholesteatoma. In their reports, atretic canal cannot prevent the development of cholesteatoma. We reviewed 4 cases of CAA associated with cholesteatoma with medical records and preoperative temporal bone CTs retrospectively. All the cases were unilaterally presented and corrected by canaloplsty. Keratin materials were demonstrated at the medial side of atretic ear canal.

Keyword

Congenital aural atresia; Cholesteatoma; Canaloplasty

MeSH Terms

Cholesteatoma*
Ear Canal
Medical Records
Retrospective Studies
Temporal Bone
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