Korean J Obstet Gynecol.
1997 Jun;40(6):1316-1320.
Congenital Absence of the Vagina and McIndoe Operation
- Affiliations
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- 1Department of Obstetrics and Gynecology, Eul-Ji General Hospital, Seoul, Korea.
Abstract
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The Mayer-Rokitanski-Kuster-Hauser Syndrome refers to the clinical entity consistingof primary amenorrhea associated with congenital absence of the vagina, 46XX Karyotype,a rudimentary uterus in the form of bilateral noncanaliculated muscular band or completeabsence, normal ovarian function and normal ovulation, normal breast development, bodyproportion and body hair, frequent associated of renal, skeletal and other congenitalanomalies. A case of Mayer-Rokitanski-Kuster-Hauser syndrome was presented and the literatureswere reviewed briefly.