Korean J Dermatol.  2002 Mar;40(3):316-318.

A Case of Congenital Smooth Muscle Hamartoma

Affiliations
  • 1Department of Dermatology, College of Medicine, Dongguk University, Dr. Lee's Skin Clinic, Kyongju, Korea. tgdljw@medigate.net
  • 2Department of Pathology, College of Medicine, Dongguk University, Dr. Lee's Skin Clinic, Kyongju, Korea.
  • 3Dr. Lee's Skin Clinic, Kyongju, Korea.
  • 4Department of Dermatology, Fatima Hospital, Taegu, Korea.

Abstract

Congenital smooth muscle hamartoma usually presents as a well-circumscribed, hypertrichotic, hyperpigmented or skin colored patch or plaque on the trunk or an extremity at birth. Histologically, numerous thick, long, well defined bundles of smooth muscle fibers are scattered throughout the dermis in various directions. We report a case of congenital smooth muscle hamartoma in an 8-month-old female infant who showed hypertrichotic, skin colored plaque on the lumbosacral area since at birth. The pseudo-Darier sign was positive. Histopathologic findings were numerous, well-defined bundles of smooth muscle fibers in the dermis (H and E, Masson-trichrome stain).

Keyword

Congenital smooth muscle hamartoma; Pseudo-Darier's sign

MeSH Terms

Dermis
Extremities
Female
Hamartoma*
Humans
Infant
Muscle, Smooth*
Parturition
Skin
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