Korean J Anesthesiol.  2006 Feb;50(2):228-231. 10.4097/kjae.2006.50.2.228.

Anesthetic Management of a Patient with Tuberous Sclerosis Undergoing Bilateral Nephrectomy: A case report

• Lee D
• Lee KC
• Kim HS
• Kwak HJ
• Moon KT

• KMID: 2237466
• DOI: http://doi.org/10.4097/kjae.2006.50.2.228

Abstract

Tuberous sclerosis is an autosomal dominantly transmitted genetic disorder that has characteristic symptoms triad of mental retardation, convulsion, and facial angiofibroma. Because it is a relatively uncommon disorder, there are few informations about anesthetic management for this disorder. We report a case of tuberous sclerosis that had involved bilateral kidneys. A 14-year old female patient was induced with thiopental sodium, rocuronium bromide and then intubated with an internal diameter 6.5 mm of reinforced tube. Anesthesia was maintained with O2-N2O-isoflurane. Surgery took 3 hours and there were no remarkable changes in vital signs and arterial blood gas analysis.

Keyword

anesthesia; nephrectomy; tuberous sclerosis

MeSH Terms

Adolescent
Anesthesia
Angiofibroma
Blood Gas Analysis
Female
Humans
Intellectual Disability
Kidney
Nephrectomy*
Seizures
Thiopental
Tuberous Sclerosis*
Vital Signs
Thiopental