Korean J Anesthesiol.  2006 Sep;51(3):371-374. 10.4097/kjae.2006.51.3.371.

Anesthesia for a Sturge-Weber Syndrome Patient with Severe Facial Hemangioma: A case report

• Chung KD
• Son YS
• Hong SH
• Cho HS

• KMID: 2237441
• DOI: http://doi.org/10.4097/kjae.2006.51.3.371

Abstract

Sturge-Weber syndrome is characterized by congenital skin angiomas throughout the facio-trigeminal region, which can cause difficulty in airway management in the case of general anesthesia. The problems with this syndrome include glaucoma, seizures, severe mental retardation, intracranial cavernous hemangioma, etc. We report a case of a patient with Sturge-Weber syndrome with severe facial hemangioma who underwent septoplasty and inferior turbinectomy under general anesthesia. We also review the literature on the anesthetic management for the Sturge-Weber syndrome and discuss methods for avoiding complications.

Keyword

Sturge-Weber syndrome; anesthetic management; difficult airway

MeSH Terms

Airway Management
Anesthesia*
Anesthesia, General
Glaucoma
Hemangioma*
Hemangioma, Cavernous
Humans
Intellectual Disability
Seizures
Skin
Sturge-Weber Syndrome*