J Korean Surg Soc.  2010 Nov;79(5):411-414. 10.4174/jkss.2010.79.5.411.

Extraskeletal Ewing's Sarcoma of the Breast, Mimicking Cyst

• Kim YS
• Lee KH
• Choi SJ
• Cho YU
• Cho SG
• Kim MY
• Kim YJ

• KMID: 2212055
• DOI: http://doi.org/10.4174/jkss.2010.79.5.411

Abstract

Extraskeletal Ewing' sarcoma (EES) is a rare soft tissue tumor morphologically indistinguishable from the osseous Ewing's sarcoma (ES). We report a case of recurrent EES of the breast that, to the best of our knowledge, has rarely been reported. It was initially confused for a cyst on ultrasound. In addition, MRI and breast-specific gamma imaging (BSGI) in our case have complementary value over conventional imaging.

Keyword

Primitive neuroectodermal tumor; Ewing's sarcoma; Breast

MeSH Terms

Breast
Neuroectodermal Tumors, Primitive
Sarcoma
Sarcoma, Ewing

Figure

• 

  Fig. 1 Primary Ewing's sarcoma of the breast in a 35-year-old woman. (A) Sonography showed a 2 cm, well-circumscribed, oval anechoic mass with posterior enhancement at the 12 o'clock position, 2 cm from the nipple. (B) Maximum intensity projection (MIP) image showed remained, smooth marginated, strong enhancing mass with increased vascularity after IV gadopentetate dimeglumine. (C) The mass showed hyperintense lesion on T2-weighted image. (D) MR spectroscopic image demonstrated elevated choline peak at 3.2 ppm. (E) Breast-specific gamma imaging (BSGI) showed hot uptake in upper inner quadrant (arrow). (F) Immunohistochemically, the lesion is composed of solid sheets of primitive or undifferentiated small round cells (H&E stain, ×200).

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