J Korean Soc Radiol.  2013 Sep;69(3):197-200. 10.3348/jksr.2013.69.3.197.

A Case Report of Congenitally Corrected Transposition of Great Arteries: Morphologic and Functional Evaluation with Cardiac CT

• Lee H
• Park BW

• KMID: 2208801
• DOI: http://doi.org/10.3348/jksr.2013.69.3.197

Abstract

Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital anomaly characterized by atrioventricular and ventriculoarterial discordance. We report a case of new-onset heart failure in a 69-year-old female in whom cardiac CT demonstrated ccTGA without the associated cardiovascular anomalies. In this case, cardiac CT was useful for elucidating the rare and unexpected congenital etiologies of abrupt-onset heart failure in an old patient by the simultaneous evaluation of cardiac morphology and function as a single study (inserted).

MeSH Terms

Aged
Arteries
Female
Heart Failure
Humans
Transposition of Great Vessels
Transposition of Great Vessels

Figure

• 

  Fig. 1 Cardiac CT performed on 69-year-old female. A. Three-dimensional volume-rendered images show spatial relationship of great arteries with ascending aorta and main pulmonary artery. Anterior descending artery (long arrow) and circumflex artery (short arrow) arise from left main coronary artery off of anterior aortic sinus. Note stair-step artifact (*) from irregular heart rhythm on mid segment of left anterior descending artery. Right coronary artery (arrowhead) originates from posterior aortic sinus. B. Curved multiplanar reformation image demonstrates anterior descending (long arrow), circumflex (short arrow), and right coronary artery (arrowhead) without luminal stenosis. Again, stair-step artifact (*) is noted on mid segment of left anterior descending artery. C, D. Diastolic (left) and systolic (right) reconstruction images clearly depict systemlic right ventricle and morphologic left ventricle on 3 dimensional volume rendering image (C) and 4 chamber view (D). E. Diastolic (left) and systolic (right) short axis reconstructions show hypertrabeculation and intertrabecular recesses filled with blood.

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