J Korean Pediatr Soc.
2000 Aug;43(8):1122-1126.
Two Cases of Left Ventricular Tumors Complicating Subaortic Stenosis in Newborn Infants
- Affiliations
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- 1Department of Pediatrics, Chonnam National University Medical School, Kwangju, Korea.
Abstract
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The most cornmon obstruction of left ventricular outflow in childhood is produced either
by a fibrous ring below the aortic valve, or by localized or diffuse muscular hypertrophy
of the inter-ventricular septum. Cardiac tumors causing subaortic stenosis in the newborn
infant are extremely rare. This report describes two cases of subaortic stenosis caused by
a tumor of the left ventricle in newborn infants, both diagnosed by 2-dimensional
echocardiography. In one patient, the obstructive portion of the tumor was successfully
resected from its attachment to the ventricular septum by aortotomy on day 5. Histologic
examination confirmed the diagnosis of rhabdomyoma. This patient developed cutaneous,
neurologic and radiologic abnormalities of tuberous sclerosis during the follow-up of 42
months.